Journal of Yeungnam Medical Science

Case Report

Spontaneous renal artery dissection in Ehlers-Danlos syndrome.: Byung Hun Lim, Song I Lee, Jae Hong Lim, Su Jin Oh, Min Su Chu, Seon Ho Ahn, Seung Jae Byun; Yeungnam Univ J Med. 2016;33(1):44-47. Published online June 30, 2016; DOI: https://doi.org/10.12701/yujm.2016.33.1.44

Abstract PDF: Primary dissection of the renal artery is rare. Spontaneous renal artery dissection can be associated with diseases such as medial degeneration, neurofibromatosis, syphilitic arteritis, tuberculosis, polyarteritis nodosa, Marfan syndrome, fibromuscular dysplasia, or Ehlers-Danlos syndrome (EDS). Among these causes, EDS related renal artery dissection is very rare worldwide and has not been previously reported in Korea. EDS are a group of heritable connective tissue disorders characterized by fragility of the skin and hypermobility of the joints. We describe the case history of a young man who presented with left side flank pain, hypermobility of the hand joints and showed left renal artery dissection on computed tomography and angiography that turned out to be the first complication of vascular type EDS.

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